the evaluation and presentation of a rare case of gonadal dysgenesis

a seventeen-years old woman was presented with infertility and primary amenorrhea. she had normal stature, femate phenotype and normal development of breasts, external genitalia, vagina and cervix. pelvic examination showed a large lobulated mass. on sonography there was a mass with probable origin of ovary. paraclinic tests were carried out. gonadotropins were in postmeno pausal limits. alpha fetoprotein, beta subunit (b-hcg) assay were normal laparotomy revealed a gonadat mass on right side, normal uterus and left streak gonad. pathologic report of tumor was dysgerminoma and teratoma. due to pathology of tumor and y chromosome, we advised the patient to remove the other streak gonad and have irradiatio